Mast Cell Leukaemia: c-KIT Mutations Are Not Always Positive

نویسندگان

  • Magalie Joris
  • Sophie Georgin-Lavialle
  • Marie-Olivia Chandesris
  • Ludovic Lhermitte
  • Jean-François Claisse
  • Danielle Canioni
  • Katia Hanssens
  • Gandhi Damaj
  • Olivier Hermine
  • Mohammed Hamidou
چکیده

Mast cell leukemia (MCL) is a rare and aggressive disease with poor prognosis and short survival time. D816V c-KIT mutation is the most frequent molecular abnormality and plays a crucial role in the pathogenesis and development of the disease. Thus, comprehensive diagnostic investigations and molecular studies should be carefully carried out to facilitate the therapeutic choice. A MCL patient's case with rare phenotypic and genotypic characteristics is described with review of major clinical biological and therapeutic approaches in MCL.

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عنوان ژورنال:

دوره 2012  شماره 

صفحات  -

تاریخ انتشار 2012